ʻO ka maʻi Antiphospholipid a me ka hāpai

ʻO ka maʻi Antiphospholipid (APS) he hui ia o nā maʻi autoimmune eʻikeʻia ana e ke kāpiliʻana o kahi maʻi nui o nā mea'elepona i nā phospholipids e waiho nei i loko o ka plasma toto (antipodholipid antibodies). I waena o nā wāhine e loaʻa ana i ka moe maʻamau , ua kiʻekiʻe ka maʻi o ka antiphospholipid syndrome, a he 28-43%. ʻO ka koi nui o kēia maʻi pilikino he thrombosis.

He aha nā kumu nui o ke kūkuluʻana i ka APS?

ʻO nā kumu o ka uluʻana o ka maʻi antiphospholipid he kakaikahi wale nō. Hiki ke hoʻomohala i kēia maʻi i nā hihia i lalo:

  1. Ke maʻi kekahi wahine i ka lupus erythematosus pūnaewele .
  2. Ke kuhi nei i ka hana hana o ka thrombosis. Ke kauʻia nā kīʻaha koko e hāʻawi i ke koko i ka'ōpū, e kūkuluʻia ka mea i kapaʻia he "abdominal toad", kahi iʻikeʻia ai keʻano o ka pihi, kaʻeha o ke kino ma ka'ōpū ma hope koke o kaʻaiʻana.
  3. Hoʻoemiʻia o nā platelets i loko o ke koko, i heleʻoleʻia me nā hanana maʻi.
  4. ʻO ka heleʻana o ka moʻolelo o kaʻeha meocardial a me nā maʻi'ē aʻe e pili ana i nā maʻi o ka loloka.

Pehea e hōʻikeʻia ai ka maʻi'ahapipopholipid?

Nā hōʻailona o ka maʻi antiphospholipid, pili pono i nā kumu he nui. No laila, koʻikoʻi nui nāʻano o kēia mau mea:

No laila, i keʻano inā he loli o nā moku liʻiliʻi, ua mālamaʻia nā kuʻi liʻiliʻi i nā hana o ke kola e hānai ana iā lākou. Eia kekahi laʻana, inā pilikia ka piko o nā liʻiliʻi liʻiliʻi, hiki i ka wā e pale ai i ka pilikino o kēlā me kēia wahi o ka myocardium, akā, inā ua paniʻia ka lumen o ke aniani keʻekeʻa, hiki i ka hōʻailona o ka meocardial.

ʻO ka manawa maʻamau o ka maʻi'alophospholipid i loko o nā wāhine hāpai e hiki iā ia ke hoʻomaʻamaʻa i nāʻano maʻi'ē aʻe, a me keʻano o nā hōʻailona. Pēlā, hiki ke hōʻikeʻia nā hōʻailona o ka maʻi o ka antiphospholipid i mua o kahi lyvedo reticular (lacy, me nā mimili o nā moku ma kaʻili o ka ili). Eia kekahi,ʻo nā maʻi ulcers e hoʻomauʻia ana, a me ka diagonary āpau, hiki ke kuhikuhi i keʻano o kēia mau maʻi i loko o ke kino.

Pehea e hanaʻia ai ka lawelawe?

Hoʻomaʻoʻia kahi maʻi'ahapipoplipid i ka'ōpūʻana e mālamaʻia ma lalo o ka mana o nā kaukaʻelua: he kaukamaika a he kaukamaika. ʻO keʻano o kēiaʻano pilikino ka hoʻohanaʻana i nā glucocorticoids a me nā cytostatics. Me ke kiʻekiʻe o nā mea'epikopoko i loko o ke koko,ʻo ka mea hoʻokahi wale nō ka hoʻoponoponoʻana i ka plasmapheresis (ka hoʻomaʻemaʻeʻana i ke koko).