ʻO Myasthenia gravis - nā hōʻailona, ​​nā kumu

ʻO kekahi o nā maʻi kaulana loaʻo myasthenia gravis. ʻO kēia maʻi e pili ana i ka neuromuscular system. ʻO nā kumu o ka myasthenia gravis keʻano likeʻole, akā, hoʻokahi nāʻano o nā maʻi o ka maʻi no ka nui o nā meaola. Hoʻopiliʻia ka maʻi me ka hoʻonuiʻia o ka luhi ma nā uala muscle. ʻO Myasthenia gravis,ʻo nā kāne a me nā wāhine, akā, e like me ka hōʻikeʻana i ka hōʻike, hoʻonui pinepine ka maʻi maikaʻi o ka maʻi.

Nā kumu o myasthenia gravis

ʻOiaiʻo ka hoʻonaʻauaoʻana i ka maʻi i hala no nā makahiki he nui,ʻo ia nō ka hoʻomakaʻana o ka myasthenia gravis,ʻaʻole hiki i nā akamai ke'ōlelo. ʻIke loa, he nui keʻano o ka predisposition pono'ī i ka uluʻana o ka maʻi. ʻO ia ke kumu e hiki ai keʻikeʻia i nā manawa i nā keiki hānau hou. Eia naʻe, ma hope o nā pule hebedoma, a me nā lā, hiki wale nō ka maʻi o nā keiki.

ʻO kekahi kumu kumu'ē aʻe o ka myasthenia gravis, he hopena o ka momona a me ka momona . I kēia hihia, loaʻa nā'epelu i loko o nāʻupena o ke kino e hōʻino ana i nā mea loaʻa i ka loaʻa o ka mea e komo ai i ka paʻakikī o nā kaha muscle. Ua hoʻokumuʻia nāʻano'epikopiko ma muli o nā maʻi e puka mai ana i loko o nā genes o nā protein. ʻO ke kumu o kēia mau mea a pau, kahi kūponoʻole ia o ka pūnaewele immune.

Nā Symptoms of myasthenia gravis

Aiaʻekolu mauʻano nui o myasthenia gravis:

Hiki i nā mea a pau ke kūpono a loaʻa paha iā lākou a alakaʻi i ka hoʻomahaʻana o nāʻiʻo i kuʻiʻia. Hanaʻia kēia ma nāʻano he nui ma hope o ka ikaika.

ʻO kaʻike nui o myasthenia gravis heʻaluaʻike. Ma keʻano like me kēia hōʻailona o ka maʻi, hikiʻole ke komoʻole i nā'ōpili. ʻO nā maka o ka mea hoʻomanawanui ua'eleʻe wikiwiki aʻe ma mua, a uaʻikeʻia kēia ma keʻano o ka māmā o nā kaumaha.

I ka hapanui o nā hihia, ma ka mua, ua kaumaha nā mīkini, a ua hānai pololeiʻia nā manaʻo o nā aʻalolo. I ka wā e hiki mai ana, no ka hoʻouluʻana o ka maʻi e hiki ke hoʻopili i nāʻiʻo o ka'ā'ī, nā lālā.

ʻO ka lōʻihi ke nohoʻole ka myasthenia gravis me ka makaʻala,ʻo ka nui o nā hōʻailona o ka maʻi. ʻO ka hōʻailona maʻamau o ka maʻiʻo ia hoʻi ka uhakiʻana i ka'ōlelo wehewehe. He nui nā maʻi ma hope o ka ikaika e pilikia ana i nā pilikia, e ho'āʻo ana e hoʻokani i kekahi mau'ōlelo a me nā hua'ōlelo maʻalahi.

Eia hou, hiki ke hoʻomaopopoʻia keʻano maʻamau, bulbar a me ocular myasthenia gravis ma nā hōʻailona o kēia mau mea:

I loko o ka myasthenia pāʻani, a me nā mea'ē aʻe, ua loli nā'ōlelo. Hiki ke kani ka leo o ka mea maʻi, kūleʻa, hoʻonanea a noho mālie. ʻO kahiʻano maʻamau o ka maʻi hele pū me ka nāwaliwali o nā puʻupuʻu. I ke kakahiaka, hiki ke hoʻomaopopoʻia ke kūlana o ka mea maʻi ma ka maikaʻi, akā, ma ke ahiahi, e piʻi mau ana.

I ka hoʻomakaʻana o ka hopena ma hope o ka hoʻomaha iki, ua hoʻi ka maʻi o ka mea maʻi i ka mea maʻamau. Akā i ka manawa lōʻihi,ʻo ka hōʻailona o ka masthenia gravis e waihoʻia ma hope o ka hoʻomaha piha.

ʻO ke kūʻana me ka maʻi, hiki i nā lāʻau lapaʻau, a me ka acetylcholine. ʻO nā mea maikaʻi loaʻo Proserin aʻo Kalimin. Eia hou, hiki ke kau i nā corticosteroids a me nā cytostatics. Inā pono, ua hoʻokuʻuʻia ka mea maʻi i ka maka o koumus.