ʻO ka fibrosis

ʻO ka meaʻoi aku ka paʻakikī e mālama i nā maʻi i hoʻopiliʻia me ka hoʻohuiʻana. ʻO nāʻano o nā maʻi e like me cystic fibrosis, a heʻoi aku ka laulā nui loa a me ka papa ola mau loa. Aia kekahi mauʻano likeʻole o kēia maʻi, ua hoʻonohonohoʻia lākou e like me ka'āpana a me keʻano o ka pohāʻana o nā'ōpū o loko.

He aha ka cystic fibrosis aiʻole cystic fibrosis?

ʻO ka maʻi i ho'ākākaʻiaʻo ka hoʻololiʻiaʻana o ka mana CFTR e pili ana i ka laweʻana o nā paʻakai. Ma muli o kona hoʻololi kūlohelohe, ua hūnāʻia ke kamepili, i hanaʻia e nāʻano momona o ke kino. Ma muli o ka lilo nui o ka paʻakai i loko o nā pūnaewele, a me ka nele i ka wai, ka paʻakikī o ke kīpona he paʻakikī a paʻa ia i loko o nā pahu, eʻokiʻia. Ma hope o kekahi manawa ma ka pūnaewele o iaʻano "traffic jam" ua hoʻokumuʻia nā kumukū.

Aia 3 mauʻano nui o cystic fibrosis:

Aia kekahi mauʻaoʻao e pili ana i ka maʻi, e like paha, aia he cystic fibrosis o ka lacteal a me ka pancreas, ka paranasal sinuses. ʻAʻole lākou iʻikeʻia, akā,ʻaʻole iʻoi aku ka maikaʻi ma mua o nāʻano o nāʻano pilikino.

Nā hōʻailona o ka cystic fibrosis

ʻO nā hōʻailona o ka cystic fibrosis e hilinaʻiʻia ma kahi o ka leona a me keʻano o ka maʻi, a me keʻano o kona maʻi.

Hōʻikeʻia ka fibrosis maʻamau o ka maʻi a penei:

ʻO ke kino'ōpū o cystic fibrosis me ka hōʻailona likeʻole:

I ka manawa pinepine, me kēiaʻano o cystic fibrosis, ua hoʻopiliʻia ke ake. No muli o ka haki o ka lawe a me ka excretion o ka bile ma loko o ka'ōpū, a ma muli o ka hopena o ke kahe o ka pele, hoʻonāukiukiʻia ka hoʻomaka o ka cirrhosis.

ʻO kaʻanoʻoi loa o ka cystic fibrosis i hui pūʻia. Hoʻohuiʻia nā hōʻailona o ka bronchopulmonary a me nā pathology digestive simultaneously.

Hanaʻia o cystic fibrosis a iʻole cystic fibrosis

He hikiʻole ke hoʻokuʻu i ka maʻi i hōʻikeʻia no ka wā pauʻole, akā naʻe, me ka hōʻailona maʻamau, ka maikaʻi o ke ola o kekahi kanaka me ka cystic fibrosis.

Hiki i nā lāʻau lapaʻau i kauohaʻia e ke kauka, pono ka hoʻonohonoho pono e hoʻonohonoho pono i ka meaʻaiʻai, hana mau i nāʻoihana kino kūikawā, nā haʻuki hauʻoli.